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Many thanks to all the patients giving their agreement to publishing pictures showing the disease.

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  26. Gelbmann CM, Köllinger M, Gmeinwieser J, Leser HG, Holstege A, Schölmerich J. Spontaneous rupture of liver in a patient with Ehlers Danlos disease type IV. Dig Dis Sci. 1997 Aug;42(8):1724–30.
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  43. Hakim AJ, Grahame R. A simple questionnaire to detect hypermobility: an adjunct to the assessment of patients with diffuse musculoskeletal pain. Int J Clin Pract. 2003 Apr;57(3):163–6.
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